Name
POEMS SYNDROME ( CROW-FUKASE SYNDROME )
DESCRIPTION
DETAIL
UNKNOWN ETIOLOGY, CONSISTS OF : POLYNEUROPATHY, ORGANOMEGALY, ENDOCRINOPATHY, MONOCLONAL COMPONENT & SKIN CHANGES. ALL SYMPTOMS ARE DUE TO PLASMA CELL DYSCRASIA* NERVE CONDUCTION TEST - BILATERAL SYMMETRICAL DISTAL SENSORIMOTOR NEUROPATHY. * ELECTROMYOGRAPHY & NERVE BIOPSY - SUGGESTIVE OF DEMYELINATION & AXONAL DEGENERATION * SERUM E2 LEVELS - ELEVATED * TSH LEVEL - RAISED IF THYROID ENVOLVEMENT * SERUM PROLACTIN LEVELS - RAISED * BLOOD SUGAR - RAISED IF DIABETES PRESENTATION
TYPENOTES
RELATED DISEASE
Not Available Disease
DISEASE
INVESTIGATION
TSH, SERUM PROLACTIN ( NONPREGNANT FEMALE ), SERUM E2 ( FEMALE ), SERUM E2 ( MALE ), COMPLETE BLOOD COUNT, ELECTROMYOGRAPHY, NERVE CONDUCTION TEST, SERUM PROLACTIN ( MALE )