Name
ANEMIA , APLASTIC
DESCRIPTION
DETAIL
D.D. : 1. PANCYTOPENIA WITH HYPOCELLULAR BONE MARROW * ACQUIRED APLASTIC ANEMIA * INHERITED APLASTIC ANEMIA ( FANCONIS ANEMIA ) * SOME MYELODYSPLASIA SYNDROME * RARE ALEUKEMIC LEUKEMIA * SOME AC LYMPHOID LEUKEMIA * SOME LYMPHOMAS OF BONE MARROW 2. PANCYTOPENIA WITH CELLULAR BONE MARROW A. PRIMARY BONE MARROW DISEASES * MYELODYSPLASIA SYNDROMES * PAROXYSMAL NOCTURNAL HAEMOGLOBINURIA * MYELOFIBROSIS * SOME ALEUKEMIC LEUKEMIA * MYELOPHTHIASIS * BONE MARROW LYMPHOMA * HAIRY CELL LEUKEMIA B. SECONDARY TO SYSTEMIC DISEASES * SLE * HYPERSPLENISM * B12, FOLATE DEFICIENCY * OVERWHELMING INFECTION * ALCOHOL * BRUCELLOSIS * SARCOIDOSIS * TUBERCULOSIS * LEISHMANIASIS 3. HYPOCELLULAR BONE MARROW WITH/ WITHOUT CYTOPENIA * Q-FEVER * LEGIONNAIRES DISEASE * ANOREXIA NERVOSA, STARVATION * MYCOBACTERIA OTHER CAUSES : * RADIATION * CHEMICALS LIKE BENZENE * DRUGS * INFECTIONS LIKE VIRAL INFECTIONS * IMMUNOLOGICAL DISEASES LIKE TRANSFUSION ASSOCIATED GRAFT VERSUS HOST DISEASE, EOSINOPHILIC FASCIITIS, SLE * PREGNANCY - SELF REMMITING DISEASEOTHER TESTS : * SMEAR SHOWS LARGE ERYTHROCYTES & PAUCITY OF PLATELETS & GRANULOCYTES, MCV - INCREASED, RETICULOCYTES - ABSENT OR FEW, LYMPHOCYTES - NORMAL OR REDUCED. PANCYTOPENIA WITH A FATTY OR EMPTY BONE MARROW. * CHROMOSOME BREAKAGE STUDIES OF PERIPHERAL BLOOD TO EXCLUDE FANCONI ANEMIA * CHROMOSOME STUDIES OF BONE MARROW CELLS MAY DIAGNOSE MYELODYSPLASIA. IT IS NEGATIVE IN APLASTIC ANEMIA. * MRI TO SEE FAT CONTENT ON FEW VERTIBRAE IN APLASTIC ANEMIA * FLOW CYTOMETRIC ASSAYS FOR THE DIAGNOSIS OF PAROXYSMAL NOCTURNAL HAEMOGLOBINURIA.
TYPENOTES
RELATED DISEASE
Not Available Disease
DISEASE
INVESTIGATION
RETICULOCYTE COUNT, BONE MARROW ASPIRATION, COMPLETE BLOOD COUNT