Name
AGALSIDASE ALFA
Mode of Action
ALPHA GALACTOSIDASE A IS AN ENDOGENOUS ENZYME THAT HYDROLYSES TERMINAL ?-D-GALACTOSE RESIDUES IN OLIGOSACCHARIDES AND GALACTOLIPIDS INTO MORE EASILY DIGESTIBLE MONO- AND DISACCHARIDES. A FORM DERIVED FROM A FUNGAL SOURCE IS USED TO PREVENT INTESTINAL GAS. AGALSIDASE ALFA AND BETA ARE RECOMBINANT FORMS OF ALPHA GALACTOSIDASE A USED FOR THE LONG-TERM ENZYME REPLACEMENT THERAPY OF FABRY DISEASE .
Dosage
AGALSIDASE ALFA IS GIVEN BY INTRAVENOUS INFUSION IN A DOSE OF 200 MICROGRAMS/KG OVER 40 MINUTES, REPEATED EVERY ALTERNATE WEEK. PT SHOULD RECIEVE SOME ANTIPYRETIC BEFORE INJECTION
Drug Group
[ENZYME] , [RECOMBINANT FORM OF ALFA GALACTOSIDASE A ENZYME]
Cross Reaction
AGALSIDASE ALFA OR BETA SHOULD NOT BE USED WITH AMIODARONE, CHLOROQUINE, MONOBENZONE, OR GENTAMICIN, WHICH ALL HAVE THE POTENTIAL TO INHIBIT INTRACELLULAR ?-GALACTOSIDASE ACTIVITY.
Drug Interaction
Drugs Side Effect
Drug Categories
Special Precaution
Drug Safety
Monograph